Primary Cardiac Angiosarcoma: A Rare Tumor

Malignant cardiac tumors are rare, with an autopsy prevalence of 0.001-0.28% [1]. Benign tumors are more common than malignant, and most initial differential diagnoses for a cardiac mass, when first detected, involve benign lesions. An angiosarcoma is a malignant neoplasm characterized by rapidly proliferating, extensively infiltrating anaplastic cells derived from blood vessels that line irregular blood-filled spaces [2]. When occurring as a cardiac primary tumor, most cases are detected late due to wide variation in presentation from asymptomatic to aggressive local recurrence and widespread metastases. A high index of suspicion must be maintained to make a diagnosis. Pathological findings and staging usually determine prognosis and therapeutic options.